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产品目录

重组人GCDH(线粒体戊二酰辅酶A脱氢酶)图片
产品货号:
JN1026
中文名称:
重组人GCDH(线粒体戊二酰辅酶A脱氢酶)
英文名称:
Recombinant Human Glutaryl-CoA Dehydrogenase, Mitochondrial
产品规格:
10μg|50μg|500μg|1mg
发货周期:
1~3天
产品价格:
询价
本品由我们的大肠杆菌表达系统制备而成,目的基因编码的Arg45-Lys438在N端含有His标签。

GCDH质量控制:>95%(还原性SDS-PAGE)

GCDH制剂:液体

GCDH保存:收到货后请置于-20℃,可保存6个月,避免反复冻融。

关于GCDH
Glutaryl-CoA Dehydrogenase Mitochondrial (GCDH) is an enzyme that acts upon glutaryl-coenzyme A, creating crotonyl-coenzyme A. It plays a role in the metabolism of lysine, hydroxylysine and tryptophan. It uses electron transfer flavoprotein as its electron acceptor. Isoform Short is inactive Glutaryl-CoA and electron-transfer flavoprotein to (E)-but-2-enoyl-CoA, CO2 and reduced electron-transfer flavoprotein. A defect in this enzyme is associated with neurological condition glutaric acidemia type 1 and cause a progressive form of early-onset generalized dystonia.
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