产品货号:
JN0953
中文名称:
重组人中链酰基辅酶A脱氢酶(ACADM)(MCAD)
英文名称:
Recombinant Human Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial
产品规格:
10μg|50μg|500μg|1mg
发货周期:
1~3天
产品价格:
询价
本品由我们的大肠杆菌表达系统制备而成,目的基因编码的Lys26-Asn421在N端含有His标签。
ACADM质量控制:>95%(还原性SDS-PAGE)
ACADM制剂:液体
ACADM保存:收到货后请置于-20℃,可保存6个月,避免反复冻融。
关于ACADM:
Medium-Chain Specific Acyl-CoA Dehydrogenase (ACADM) is a mitochondrial fatty acid beta-oxidation that belongs to the acyl-CoA dehydrogenase family. ACADM is a homotetramer enzyme that catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. ACADM is specific for acyl chain lengths of 4 to 16. It is essential for converting these particular fatty acids to energy, especially during fasting periods. Defects in ACADM cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death.
相关搜索:重组人中链酰基辅酶A脱氢酶(ACADM)(MCAD)
ACADM质量控制:>95%(还原性SDS-PAGE)
ACADM制剂:液体
ACADM保存:收到货后请置于-20℃,可保存6个月,避免反复冻融。
关于ACADM:
Medium-Chain Specific Acyl-CoA Dehydrogenase (ACADM) is a mitochondrial fatty acid beta-oxidation that belongs to the acyl-CoA dehydrogenase family. ACADM is a homotetramer enzyme that catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. ACADM is specific for acyl chain lengths of 4 to 16. It is essential for converting these particular fatty acids to energy, especially during fasting periods. Defects in ACADM cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death.
相关搜索:重组人中链酰基辅酶A脱氢酶(ACADM)(MCAD)