产品货号：
Z25643
中文名称：
SACS抗体
英文名称：
Anti-SACS Antibody
产品规格：
50μl|100μl|150μl
发货周期：
1～3天
产品价格：
询价
| 抗体名称 | Anti-SACS Antibody |
| 指标别名 | sacsin molecular chaperone;ARSACS;DNAJC29;PPP1R138;SPAX6 |
| 克隆性 | Polyclonal |
| 检验物种 | human,mouse,rat |
| 应用范围 | WB,IHC,ELISA |
| 基因名称 | SACS |
| 抗体来源 | Rabbit |
| 抗体类型 | IgG |
| 免疫原 | E.coli-derived human Sacsin recombinant protein (Position:E3709-L3909). |
| 实际分子量 | 521KD |
| 成分 | 500μg/mL antibody with PBS，0.02% NaN3,1mg BSA and 50% glycerol. |
| 纯化方式 | Immunogen affinity purified. |
| 浓度 | 500μg/mL |
| 产品形态 | 溶液 |
| 保存条件 | 12 months from date of receipt，-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing. |
| 背景资料 | Sacsin also known as DnaJ homolog subfamily C member 29 (DNAJC29) is a protein that in humans is encoded by the SACS gene.This gene consists of nine exons including a gigantic exon spanning more than 12.8k bp.It encodes the sacsin protein,which includes a UBQ region at the N-terminus,a HEPN domain at the C-terminus and a DnaJ region upstream of the HEPN domain.This modular protein is essential for normal mitochondrial network organization.The gene is highly expressed in the central nervous system,also found in skin,skeletal muscles and at low levels in the pancreas.Mutations in this gene result in autosomal recessive spastic ataxia of Charlevoix-Saguenay (ARSACS),a neurodegenerative disorder characterized by early-onset cerebellar ataxia with spasticityand peripheral neuropathy. |
| Uniprot ID | Q9NZJ4 |
| 推荐配套试剂 | Biorab recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ZN1926) for Western blot,and HRP Conjugated anti-Rabbit IgG Super Vision Assay Kit (ZN1865) for IHC(P).*Blocking peptide可以联系我们购买。 |
| 推荐稀释比 | Western blot(WB) 1:500～2000 Immunohistochemistry in paraffin section (IHC) 1:50～400 (ELISA)： 1:100～1000 (Boiling the paraffin sections in 10mM citrate buffer,pH6.0,or PH8.0 EDTA repair liquid for 20 mins is required for the staining of formalin/paraffin sections.) Optimal working dilutions must be determined by end user. |
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