
产品货号:
Z16822
中文名称:
GNS抗体
英文名称:
Anti-GNS Antibody
产品规格:
50μl|100μl|150μl
发货周期:
1~3天
产品价格:
询价
抗体名称 | Anti-GNS Antibody |
指标别名 | G6S,Glucosamine 6 sulfatase,GNS |
克隆性 | Polyclonal |
检验物种 | human,mouse,rat |
应用范围 | WB,ELISA |
基因名称 | GNS |
抗体来源 | Rabbit |
抗体类型 | IgG |
免疫原 | E.coli-derived human GNS recombinant protein (Position:W238-R355). |
实际分子量 | 62KD |
成分 | 500μg/mL antibody with PBS,0.02% NaN3,1mg BSA and 50% glycerol. |
纯化方式 | Immunogen affinity purified. |
浓度 | 500μg/mL |
产品形态 | 溶液 |
保存条件 | 12 months from date of receipt,-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing. |
背景资料 | N-acetylglucosamine-6-sulfatase,also known as glucosamine (N-acetyl)-6-sulfatase,is an enzyme that in humans is encoded by the GNS gene.The product of this gene is a lysosomal enzyme found in all cells.It is involved in the catabolism of heparin,heparan sulphate,and keratan sulphate.Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome).Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |
Uniprot ID | P15586 |
推荐配套试剂 | Biorab recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ZN1926) for Western blot,and HRP Conjugated anti-Rabbit IgG Super Vision Assay Kit (ZN1865) for IHC(P).*Blocking peptide可以联系我们购买。 |
推荐稀释比 | Western blot(WB) 1:500~2000 (ELISA): 1:100~1000 |
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